Cardiomyopathy: Difference between revisions

Click [http://www.cardiogenetica.nl/index.php?menuID=2 '''here'''] for detailed information on various cardiomyopathy. Listed below are the main disorders and their characteristics with examples.

!Condition  

*Fibrofatty degeneration of the RV .

*Myocardial degeneration leads to RV dilation and poor RVF .

*Preserved systolic LV function ( EF normal or slightly decreased)

*May include associated with sudden cardiac death due to ventricular fibrillation, an increased risk of thromboembolism.

*Heart failure can be caused by the rigidity of the thickened heart muscle (diastolic heart failure), by an obstruction in the LVOT (SAM ) is associated with mitral valvular insufficiency. The course of the disease is progressive.

|Non - compaction cardiomyopathy ( NCCMP )

 

LVwand has a spongy appearance .

Jenni criteria ( Heart 2007) .

Also called insulated non compaction of the ventricular myocardium ( INVM ) , is a rare form of congenital heart disease in which the tissue of the ventricular myocardium is constructed in terms of texture well.

 After HCM DCM and the most common cause of primary cardiomyopathy in children.

It is a congenital defect , which occurs in the 20th week of pregnancy .

The condition is expressed by heart failure, arrhythmias, and an increased risk of thrombus formation.

The disorder often manifests itself later in life and has a high mortality rate due to heart failure and arrhythmias .

NCCMP with crypts and apical midventriculair

NCCCMP on PSax

restrictive cardiomyopathy

 

Stiffened myocardium.

This form comes after at least 1 and is usually associated with storage diseases , such as sarcoidosis , amyloidosis , and the like.

Preserved systolic LVF . LV is not dilated .

Diastolic dysfunction ( see fig.)

LV and RV may be hypertrophied .

Dilated atria and VCI .

Pulmonary hypertension .

Myocardial echo during and amyloidosis speckled

Abnormally low É in restrictive cmp

Tako- tsubo cardiomyopathy

Tako- tsubo are octopus lure often used in Japan .

Apical ballooning , akinesia of the apex. This gives the LV configuration octopus lure .

manifests itself as an acute myocardial infarction with ST elevations , however, no significant coronary artery disease.

Is more common in women than in men , the average age of 62 to 75 years .

Stressgeïnduceerd , is triggered by an acute illness or intense emotional or physical stress

Also called "broken heart syndrome" or " Stress CMP " called .

LV normalized to several weeks in few days .

Apical ballooning

 

#1 [http://www.uptodate.com/contents/echocardiographic-recognition-of-cardiomyopathies?source=search_result&search=cardiomyopathy+echo&selectedTitle=1~150| Echocardiographic recognition of cardiomyopathies]