Cardiomyopathy: Difference between revisions

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 Click [http://www.cardiogenetica.nl/index.php?menuID=2 '''here'''] for detailed information on various cardiomyopathy. Listed below are the main disorders and their characteristics with examples.
+{| class="wikitable" cellpadding="0" cellspacing="0" border="0"
+|-
+!Condition
+!Features
+!Example
+|-
+Arrythmogene right ventricular cardiomyopathy (ARVC)
+Fibro - fatty degeneration" of the RV .
+Myocardial degeneration leads to RV dilation and poor RVF .
+Ventricular fibrillation by slow conduction velocities , guide block and spatial variation in conduction velocity .
+Aneurysms of the RV free wall .
+Echo Dens moderator band and myocardial RV free wall .
+genetic component
+Rare 1 : 5000 people.
+Echodense RV free wall for suspected ARVC
+ARVCstrain
+Decreased RV strain in ARVC
+Dilated cardiomyopathy ( DCM )
+It is the most common form of cardiomyopathy.
+Also known as congestive cardiomyopathy called
+Poor LVF and LV dilatation .
+Arrhythmias ( atrial fibrillation 20-30 % ) .
+Clot formation, which may lead to thrombo -embolic complications.
+Often accompanied by pulmonary hypertension , dilation of other compartments , and an insufficiency of mitral and / or tricuspid valve
+Familial DCM 's common to autosomal dominant, autosomal recessive and sex-linked inheritance .
+causes:
+( post - ) infectious : various viruses and bacteria , as the final stage of myocarditis.
+intoxication : cocaine, alcohol abuse .
+iatrogenic : some chemostatica , X-ray radiation .
+Metabolic : vitamin B1 deficiency .
+- idiopathic : In approximately 30 % of cases, no cause is found .
+DCM
+Dilated LV on AP4CH
+DCMplax
+Dilated LV on Plax
+EPSS
+EPSS is a useful measurement at follow up DCM
+Hypertrophic cardiomyopathy ( HCM )
+% Asymmetric hypertrophy of the myocardium, usually ventricular septum sometimes apical involvement .
+% Symmetrical hypertrophy of the myocardium ( not to be confused with Aortic stenosis or hypertension ) .
+Small LV lumen .
+Preserved systolic LV function ( EF normal or slightly decreased)
+Diastolic dysfunction .
+Autosomal dominant progressive deviation from nature .
+May include associated with sudden cardiac death due to ventricular fibrillation , an increased risk of thromboembolism .
+Heart failure can be caused by the rigidity of the thickened heart muscle ( diastolic heart failure ) , by an obstruction in the LVOT (SAM ) is associated with mitral valvular insufficiency . The course of the disease is progressive .
+Occurs in persons 1:500-1000
+asympHCM
+asymmetric hypertrophy
+HCM
+symmetrical hypertrophy
+apicaleHCM
+apical hypertrophy
+Non - compaction cardiomyopathy ( NCCMP )
+LVwand has a spongy appearance .
+Jenni criteria ( Heart 2007) .
+Also called insulated non compaction of the ventricular myocardium ( INVM ) , is a rare form of congenital heart disease in which the tissue of the ventricular myocardium is constructed in terms of texture well.
+ After HCM DCM and the most common cause of primary cardiomyopathy in children.
+It is a congenital defect , which occurs in the 20th week of pregnancy .
+The condition is expressed by heart failure, arrhythmias, and an increased risk of thrombus formation.
+The disorder often manifests itself later in life and has a high mortality rate due to heart failure and arrhythmias .
+NCCMP
+NCCMP with crypts and apical midventriculair
+NCCCMP on PSax
+restrictive cardiomyopathy
+Stiffened myocardium.
+This form comes after at least 1 and is usually associated with storage diseases , such as sarcoidosis , amyloidosis , and the like.
+Preserved systolic LVF . LV is not dilated .
+Diastolic dysfunction ( see fig.)
+LV and RV may be hypertrophied .
+Dilated atria and VCI .
+Pulmonary hypertension .
+Myocardial echo during and amyloidosis speckled
+restr_cmp_TVI
+Abnormally low É in restrictive cmp
+Tako- tsubo cardiomyopathy
+Tako- tsubo are octopus lure often used in Japan .
+Apical ballooning , akinesia of the apex. This gives the LV configuration octopus lure .
+manifests itself as an acute myocardial infarction with ST elevations , however, no significant coronary artery disease.
+Is more common in women than in men , the average age of 62 to 75 years .
+Stressgeïnduceerd , is triggered by an acute illness or intense emotional or physical stress
+Also called "broken heart syndrome" or " Stress CMP " called .
+LV normalized to several weeks in few days .
+takotsubocmp
+Apical ballooning
+|}
 ==References==