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Cardiomyopathy: Difference between revisions
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!rowspan="4" valign="top"|Arrythmogene right ventricular cardiomyopathy (ARVC) | !rowspan="4" valign="top"|Arrythmogene right ventricular cardiomyopathy (ARVC) | ||
|rowspan="4" valign="top"| | |rowspan="4" valign="top"| | ||
*Fibrofatty degeneration of the RV . | *Fibrofatty degeneration of the RV. | ||
*Myocardial degeneration leads to RV dilation and poor RVF . | *Myocardial degeneration leads to RV dilation and poor RVF. | ||
*Ventricular fibrillation by slow conduction velocities, guide block and spatial variation in conduction velocity. | *Ventricular fibrillation by slow conduction velocities, guide block and spatial variation in conduction velocity. | ||
*Aneurysms of the RV free wall. | *Aneurysms of the RV free wall. | ||
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*35% symmetrical hypertrophy of the myocardium (not to be confused with aortic stenosis or hypertension). | *35% symmetrical hypertrophy of the myocardium (not to be confused with aortic stenosis or hypertension). | ||
*Small LV lumen. | *Small LV lumen. | ||
*Preserved systolic LV function ( EF normal or slightly decreased) | *Preserved systolic LV function (EF normal or slightly decreased) | ||
*Diastolic dysfunction. | *Diastolic dysfunction. | ||
*Autosomal dominant progressive deviation from nature. | *Autosomal dominant progressive deviation from nature. | ||
* | *Could be associated with sudden cardiac death due to ventricular fibrillation, an increased risk of thromboembolism. | ||
*Heart failure can be caused by the rigidity of the thickened heart muscle (diastolic heart failure), by an obstruction in the LVOT (SAM ) is associated with mitral valvular insufficiency. The course of the disease is progressive. | *Heart failure can be caused by the rigidity of the thickened heart muscle (diastolic heart failure), by an obstruction in the LVOT (SAM) and is associated with mitral valvular insufficiency. The course of the disease is progressive. | ||
*Occurs in persons 1:500-1000 | *Occurs in persons 1:500-1000 | ||
|[[Image:Asym.cmp1.jpg|400px]] | |[[Image:Asym.cmp1.jpg|400px]] | ||
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!Apical hypertrophy | !Apical hypertrophy | ||
|- | |- | ||
|Non - compaction cardiomyopathy ( NCCMP ) | |Non - compaction cardiomyopathy (NCCMP) | ||
LVwand has a spongy appearance . | LVwand has a spongy appearance. | ||
Jenni criteria ( Heart 2007) . | Jenni criteria (Heart 2007). | ||
Also called insulated non compaction of the ventricular myocardium ( INVM ) , is a rare form of congenital heart disease in which the tissue of the ventricular myocardium is constructed in terms of texture well. | Also called insulated non compaction of the ventricular myocardium (INVM), is a rare form of congenital heart disease in which the tissue of the ventricular myocardium is constructed in terms of texture well. | ||
After HCM DCM and the most common cause of primary cardiomyopathy in children. | After HCM DCM and the most common cause of primary cardiomyopathy in children. | ||
It is a congenital defect , which occurs in the 20th week of pregnancy . | It is a congenital defect, which occurs in the 20th week of pregnancy. | ||
The condition is expressed by heart failure, arrhythmias, and an increased risk of thrombus formation. | The condition is expressed by heart failure, arrhythmias, and an increased risk of thrombus formation. | ||
The disorder often manifests itself later in life and has a high mortality rate due to heart failure and arrhythmias . | The disorder often manifests itself later in life and has a high mortality rate due to heart failure and arrhythmias. | ||
NCCMP | NCCMP | ||
NCCMP with crypts and apical midventriculair | NCCMP with crypts and apical midventriculair | ||
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Stiffened myocardium. | Stiffened myocardium. | ||
This form comes after at least 1 and is usually associated with storage diseases , such as sarcoidosis , amyloidosis , and the like. | This form comes after at least 1 and is usually associated with storage diseases, such as sarcoidosis, amyloidosis, and the like. | ||
Preserved systolic LVF . LV is not dilated . | Preserved systolic LVF. LV is not dilated. | ||
Diastolic dysfunction ( see fig.) | Diastolic dysfunction (see fig.) | ||
LV and RV may be hypertrophied . | LV and RV may be hypertrophied. | ||
Dilated atria and VCI . | Dilated atria and VCI. | ||
Pulmonary hypertension . | Pulmonary hypertension. | ||
Myocardial echo during and amyloidosis speckled | Myocardial echo during and amyloidosis speckled | ||
restr_cmp_TVI | restr_cmp_TVI | ||
Abnormally low É in restrictive cmp | Abnormally low É in restrictive cmp | ||
Tako- tsubo cardiomyopathy | Tako- tsubo cardiomyopathy | ||
Tako- tsubo are octopus lure often used in Japan . | Tako- tsubo are octopus lure often used in Japan. | ||
Apical ballooning , akinesia of the apex. This gives the LV configuration octopus lure . | Apical ballooning, akinesia of the apex. This gives the LV configuration octopus lure. | ||
manifests itself as an acute myocardial infarction with ST elevations , however, no significant coronary artery disease. | manifests itself as an acute myocardial infarction with ST elevations, however, no significant coronary artery disease. | ||
Is more common in women than in men , the average age of 62 to 75 years . | Is more common in women than in men, the average age of 62 to 75 years. | ||
Stressgeïnduceerd , is triggered by an acute illness or intense emotional or physical stress | Stressgeïnduceerd, is triggered by an acute illness or intense emotional or physical stress | ||
Also called "broken heart syndrome" or " Stress CMP " called . | Also called "broken heart syndrome" or " Stress CMP " called. | ||
LV normalized to several weeks in few days . | LV normalized to several weeks in few days. | ||
takotsubocmp | takotsubocmp | ||
Apical ballooning | Apical ballooning | ||